Diagnosis: Mondini dysplasia
نویسندگان
چکیده
منابع مشابه
Peripheral vestibular pathology in Mondini dysplasia.
OBJECTIVES/HYPOTHESIS In this study, our objective was to histopathologically analyze the peripheral vestibular system in patients with Mondini dysplasia. STUDY DESIGN Comparative human temporal bone study. METHODS We assessed the sensory epithelium of the human vestibular system with a focus on the number of type I and type II hair cells, as well as the total number of hair cells. We compa...
متن کاملRecurrent Bacterial Meningitis in a Child with Mondini Dysplasia
Mondini dysplasia, also known as Mondini malformation, is a developmental abnormality of the inner and middle ears that can cause hearing loss, cerebrospinal fluid (CSF) leakage, and recurrent bacterial meningitis (RBM), which is defined as two or more episodes of meningitis separated by a period of convalescence and the complete resolution of all signs and symptoms. An accurate diagnosis of th...
متن کاملCASE REPORT Recurrent meningitis and Mondini dysplasia: A case report
esis of the inner ear. The malformation, commonly associated with deafness, is frequently heralded by meningitis secondary to communication of the middle ear with the subarachnoid space. Early recognition and successful repair of the cerebrospinal fluid leak is important to avoid the sequelae or repeated episodes of meningitis. We report a case of a 5-year-old girl in whom Mondini dysplasia pre...
متن کاملCerebrospinal fluid otorrhea and recurrent bacterial meningitis in a pediatric case with Mondini dysplasia.
Mondini dysplasia is a congenital malformation of the inner ear, which is characterized by a short and large cochlear canal of 1.5 turn rather than 2.5 turns and an apical region with cystic dilatation. Patients present with congenital deafness, when both cochlea are affected. Unilateral disease may cause recurrent meningitis, otorrhea or rhinorrhea. In this article, we report a three-year-old ...
متن کاملSensorineural hearing loss and Mondini dysplasia caused by a deletion at locus DFN3.
OBJECTIVE To study a family with inner ear malformations and sensorineural hearing loss. DESIGN Clinical, radiological, and genetic study of the members of a family with different degrees of sensorineural hearing loss. RESULTS The males in the family manifested profound congenital hearing loss with severe inner ear malformations, while the only affected female had progressive hearing loss t...
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ژورنال
عنوان ژورنال: Annals of Saudi Medicine
سال: 2006
ISSN: 0256-4947,0975-4466
DOI: 10.5144/0256-4947.2006.163